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Smith-Magenis Syndrome: Maladaptive Behaviors and Effects on Parent Stress, Coping, and Family Adjustment

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dc.contributor.advisor Rojahn, Johannes
dc.contributor.author Morse, Rebecca S.
dc.creator Morse, Rebecca S.
dc.date 2011-07-05
dc.date.accessioned 2011-08-22T18:54:55Z
dc.date.available NO_RESTRICTION en_US
dc.date.available 2011-08-22T18:54:55Z
dc.date.issued 2011-08-22
dc.identifier.uri https://hdl.handle.net/1920/6609
dc.description.abstract Smith Magenis Syndrome (SMS) is a rare genetic syndrome most commonly caused by a microdeletion on chromosome 17 p11.2. It is associated with a pattern of physical, developmental and behavioral characteristics including intellectual disability, sleep disturbance, and a variety of behavior problems. Data were collected on 25 individuals with SMS, 10 males (mean IQ 72; SD 13), and 15 females (mean IQ 68; SD 22.2); ages 1.4-19.4 (mean 6.56; SD 4.71). Parent reports were obtained using the Vineland Adaptive Behavior Scale (VABS; Sparrow, Balla, & Cicchetti, 1984), the Achenbach Child Behavior Checklist (CBCL; Achenbach, 1991), the Family Assessment Device-General Functioning Scale (Epstein, Baldwin, & Bishop, 1983), the Family Crisis Oriented Personal Evaluation Scales (McCubin, Olson, & Larson, 1991), the Parental Stress Index-3rd edition (Abidin, 1995), and the Stress Index for Parents of Adolescents (Abidin, 1995). We found positive linear relationships between maladaptive behaviors and parent stress, but no association between maladaptive behaviors and overall life stress. We also found that parent stress levels were not associated with measures of family adjustment or specific parent coping strategies.
dc.language.iso en_US en_US
dc.subject Developmental en_US
dc.subject Syndrome en_US
dc.subject Behavior en_US
dc.subject Disabilities en_US
dc.title Smith-Magenis Syndrome: Maladaptive Behaviors and Effects on Parent Stress, Coping, and Family Adjustment en_US
dc.type Dissertation en
thesis.degree.name PhD in Psychology en_US
thesis.degree.level Doctoral en
thesis.degree.discipline Psychology en
thesis.degree.grantor George Mason University en


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